Protein and calorie intakes in adult and pediatric subjects with urea cycle disorders participating in clinical trials of glycerol phenylbutyrate

Debra Hook, George A. Diaz, Brendan Lee, James Bartley, Nicola Longo, William Berquist, Cynthia Le Mons, Ingrid Rudolph-Angelich, Marty Porter, Bruce F. Scharschmidt, Masoud Mokhtarani

Research output: Contribution to journalArticlepeer-review

Original languageEnglish
Pages (from-to)34-40
Number of pages7
JournalMolecular Genetics and Metabolism Reports
Volume6
DOIs
StatePublished - Mar 2016
Externally publishedYes

ASJC Scopus Subject Areas

  • Molecular Biology
  • Genetics
  • Endocrinology

Keywords

  • Dietary management
  • Inherited metabolic disorders
  • Phenylbutyrate
  • Protein intake
  • Urea cycle disorders

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