TY - JOUR
T1 - Connective Tissue Disease-Related Interstitial Lung Disease
T2 - Prevalence, Patterns, Predictors, Prognosis, and Treatment
AU - Jeganathan, Niranjan
AU - Sathananthan, Matheni
N1 - Publisher Copyright:
© 2020, Springer Science+Business Media, LLC, part of Springer Nature.
PY - 2020/10/1
Y1 - 2020/10/1
N2 - Interstitial lung disease is a common pulmonary manifestation of connective tissue diseases and results in significant morbidity and mortality. Although all connective tissue diseases are linked by underlying autoimmunity, there is significant variability in the presentation and clinical course of interstitial lung disease associated with the different types of connective tissue diseases. In this paper, we review the prevalence, patterns, predictors, and prognosis of interstitial lung disease secondary to the most common forms of connective tissue diseases. We have also highlighted the available evidence regarding treatment options for interstitial lung disease due to different connective tissue diseases.
AB - Interstitial lung disease is a common pulmonary manifestation of connective tissue diseases and results in significant morbidity and mortality. Although all connective tissue diseases are linked by underlying autoimmunity, there is significant variability in the presentation and clinical course of interstitial lung disease associated with the different types of connective tissue diseases. In this paper, we review the prevalence, patterns, predictors, and prognosis of interstitial lung disease secondary to the most common forms of connective tissue diseases. We have also highlighted the available evidence regarding treatment options for interstitial lung disease due to different connective tissue diseases.
KW - Connective tissue disease
KW - Interstitial lung disease
KW - Myositis
KW - Rheumatoid arthritis
KW - Sjögren’s syndrome
KW - Systemic sclerosis
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U2 - 10.1007/s00408-020-00383-w
DO - 10.1007/s00408-020-00383-w
M3 - Article
C2 - 32780179
SN - 0341-2040
VL - 198
SP - 735
EP - 759
JO - Lung
JF - Lung
IS - 5
ER -